Bazex Syndrome*
نویسندگان
چکیده
Acrokeratosis Paraneoplastica or Bazex syndrome is a dermatologic manifestation usually associated with the diagnosis of squamous cell carcinoma of the upper aerodigestive tract. We report a case with exuberant clinical manifestations, exemplifying the typical cutaneous lesions in this rare syndrome, in a patient with squamous cell carcinoma of the esophagus.
منابع مشابه
Bazex-Dupre-Christol syndrome: A case report
Bazex-Dupre-Christol (BDC) syndrome is clinically characterizedby multiple basal cell carcinomas of the face that mainly occurduring the second and third decade of life, follicular atrophodermapredominantly of the dorsum sides of the hands and feetand generalized hypotrichosis; sometimes with pili torti andtrichorrhexis nodosa. Features commonly associated with BDCare milia, hypohidrosis and ca...
متن کاملCase Report: Bazex Syndrome Associated With Pulmonary Adenocarcinoma
Bazex syndrome, a rare paraneoplastic syndrome characterized by psoriasiform eruptions, palmoplantar keratosis, and symmetric onychodystrophy, is most prevalent with squamous cell carcinomas of the upper aerodigestive tract.Here, we reported an uncommon case of Bazex syndrome about an 83-year-old man with pulmonary adenocarcinoma and osseous metastasis, Physical examination found psoriasiform e...
متن کاملBazex-syndrome with esophageal cancer
We differentiate cutaneous paraneoplasias in facultative such as erythema gyratum repens and obligate such as acrokeratosis paraneoplastica. The latter is also known as Bazex-syndrome. Bazex et al. described the syndrome in 1965 in a patient with a larynx tumor [2]. In 75% of cases Bazex-syndrome develops before the diagnosis of malignancies. Its diagnosis should lead to a detailed search for c...
متن کامل[Pulmonary adenocarcinoma and Bazex syndrome (paraneoplastic acrokeratosis)].
Bazex syndrome, or paraneoplastic acrokeratosis, is a rare psoriasis-like paraneoplastic skin disease, characterized by erythema and scaling, which is accompanied by hyperkeratotic lesions. The tumors most frequently associated with Bazex syndrome are squamous cell carcinomas of the upper respiratory and digestive tracts, whereas lung cancers, particularly adenocarcinomas, are rarely associated...
متن کاملCancer Prone Disease Section
Inheritance Bazex-Dupré-Christol syndrome is an X-linked dominant genodermatosis, with a prevalence below 1/1 000 000. The female to male ratio reaches the expected 2:1, and females appear to be less affected than males. There is intrafamilial and interfamilial phenotypic variability (Lacombe and Taïeb, 1995; Kidd et al., 1996). Most cases are European patients. Oley syndrome (Oley et al., 1992...
متن کاملBazex Syndrome with Hypoalbuminemia and Severe Ascites
Bazex syndrome is a rare paraneoplastic dermatosis. The underlying malignancy frequently is squamous cell carcinoma of the upper aerodigestive tract or cervical lymph nodes from an unknown primary site. We report a 63-year-old man with squamous cell carcinoma of cervical lymph nodes from an unknown primary site. He developed a mass on the right side of his neck, cutaneous lesions diagnosed as B...
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